See Also: Hirschsprung's disease(dictionary)
Disease, Hirschsprung(health)
disease, Hirschsprung's(medicine)
Hirschsprung's disease(health)
Hirschsprung's disease(medicine)
Herbal medicine (botanical medicine, herbology, phytomedicine)(health)
Hirschsprung, Harald(medicine)
Medicine Lodge Memorial Hospital- Medicine Lodge(health)
Orthomolecular medicine (orthomolecular nutritional medicine, orthomolecular therapy)(health)
medicine(dictionary)

Hirschsprung's disease (medicine)


Hirschsprung's disease
<disease> A congenital condition which results in an enlarged and poorly functioning colon due to abnormal intestinal motility. These patients are at risk for intestinal obstruction. Constipation, vomiting, abdominal distention, poor weight gain, a retarded growth are common. Treatment include the use of a temporary colostomy with later resection of the affected portion of bowel.

Symptoms are eliminated in up to 90% of patients after surgery. Outcomes are better with early intervention.

<radiology> Aganglionosis of myenteric plexus of colon, functional obstruction, aganglionic segment of normal caliber, continuous involvement, from rectum proximally, males (80%), usually presents by 6 weeks, complications: enterocolitis, perforation, associated with Down syndrome Differential diagnosis: ileal atresia, meconium ileus (no air-fluid levels)