See Also: bullous congenital ichthyosiform erythroderma(medicine)
congenital ichthyosiform erythroderma(medicine)
ichthyosiform erythroderma, congenital(medicine)
nonbullous congenital ichthyosiform erythroderma(medicine)
Ichthyosiform erythroderma(medicine)
Herbal medicine (botanical medicine, herbology, phytomedicine)(health)
Erythroderma(medicine)
erythroderma exfoliativa(medicine)
Sezary erythroderma(medicine)
erythroderma desquamativum(medicine)

bullous congenital ichthyosiform erythroderma (medicine)


bullous congenital ichthyosiform erythroderma


Diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterised by generalised epidermolytic hyperkeratosis and autosomal dominant inheritance.

See: epidermolytic hyperkeratosis.

Synonym: generalised epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix.