See Also: leukocyte-adhesion deficiency syndrome(medicine)
leukocyte adhesion deficiency(medicine)
receptors, leukocyte-adhesion(medicine)
endothelial-leukocyte adhesion molecule(medicine)
Activated leukocyte cell adhesion molecule(health)
antibody deficiency syndrome(medicine)
17-hydroxylase deficiency syndrome(medicine)
polyendocrine deficiency syndrome(medicine)
carbonic anhydrase II deficiency syndrome(medicine)
abdominal muscle deficiency syndrome(medicine)

leukocyte-adhesion deficiency syndrome (medicine)


leukocyte-adhesion deficiency syndrome
<syndrome> Rare, autosomal recessive disorder caused by deficiency of the beta 2 integrin receptors (receptors, leukocyte-adhesion) comprising the CD11/CD18 family of glycoproteins. The syndrome is characterised by abnormal adhesion-dependent functions, especially defective tissue emigration of neutrophils, leading to recurrent infection.