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phosphogalactoisomerase (medicine)


phosphogalactoisomerase -->
udpglucose-hexose-1-phosphate uridylyltransferase
<enzyme> An enzyme that catalyses the transfer of ump from udpglucose to galactose 1-phosphate, forming udpgalactose and glucose 1-phosphate. Deficiency in this enzyme is the major cause of galactosaemia.

Chemical name: UDPglucose:alpha-D-galactose-1-phosphate uridylyltransferase

Registry number: EC 2.7.7.12